What is the primary characteristic of Arrhythmogenic cardiomyopathy?

The primary characteristic of Arrhythmogenic cardiomyopathy is the replacement of myocardial cells with fibrofatty tissue. This condition, which is often inherited, primarily affects the right ventricle and can lead to significant electrical disturbances in the heart. The fibrofatty replacement disrupts the normal structure and function of the heart muscle, leading to an increased risk of arrhythmias, heart failure, and sudden cardiac death.

The process of replacement by fibrofatty tissue can lead to the thinning of the heart walls and subsequent scarring, further compromising cardiac function. This transformation is a hallmark feature of this specific type of cardiomyopathy and is a key factor in both diagnosis and understanding the clinical implications of the condition.

The other choices mention aspects that may be related but do not capture the defining pathological feature that characterizes Arrhythmogenic cardiomyopathy.